| GENE NAME | MLH3 |
| CHROMOSOME | 14 |
| ENSEMBL ID | ENSG00000119684 |
| ENTREZ ID | 27030 |
| UNIPROT ACCESSION NUMBER | Q9UHC1 |
| GO MOLECULAR FUNCTION | protein binding; ATP hydrolysis activity; satellite DNA binding; chromatin binding; centromeric DNA binding; ATP binding; mismatched DNA binding |
| ESSENTIAL IN MOUSE | Non-essential |
| PATHWAYS | R-HSA-1500620; R-HSA-1474165; R-HSA-912446; hsa03430; R-HSA-1640170 |
| 2 combinations linked to MLH3 | OLI1068; OLI1039 |
| 2 variants linked to MLH3 | MLH3:c.3466G>A, p.Val1156Ile; MLH3:c.3943G>A, p.Glu1315Lys |
| 1 disease linked to MLH3 | Primary ovarian failure |